KMID : 0882419970520030429
|
|
Korean Journal of Medicine 1997 Volume.52 No. 3 p.429 ~ p.436
|
|
Wilson`s Disease with Abnormal Secretion of Pituitary Hormones
|
|
Kim Dae-Hyeon
Lee Dong-Uk
Lee Chang-Ki Lee Sang-Mun
|
|
Abstract
|
|
|
Wilson`s disease is a hereditary disorder in hepatic excretion of copper that results in toxic accumulations of the metal in liver, brain and other organs. Though there have been some reports of Wilson¡¯s disease with hepatic, neurologic, psychiatric symptoms, or hemolytic anemia, a case of Wilson¡¯s disease with abnormal secretion of pituitary hormones is, to our best knowledge, the first report in Korea. We report a case of Wilson`s disease with abnormal secretion of pituirary hormones, chronic active hepatitis with feature of early cirrhosis and hemolytic anemia in 18-year-old man showing delayed puberty. And also we describe a case of successful desensitization to penicillamine in a penicillamine hypersensitivity.
|
|
KEYWORD
|
|
|
|
FullTexts / Linksout information
|
|
|
|
Listed journal information
|
|
|